End-Stage Chronic Intestinal Pseudo-Obstruction Resulting in Intestinal Pneumatosis

Chronic intestinal pseudo-obstruction (CIPO) is a rare gastrointestinal motility disorder that presents with symptoms, physical exam, and imaging findings of mechanical bowel obstruction without an anatomical obstruction. Multiple etiologies, including enteric or extrinsic neuropathic dysfunction, myopathic dysfunction the interstitial cells Cajal, cause CIPO’s pathogenesis. The presentation CIPO may be idiopathic caused by underlying diseases. most common abdominal pain, bloating, distension. Here, we present patient end-stage case who failed medical therapy. Her distension progressed over decade, requiring emergency surgery due to pneumatosis.